BILATERAL PERSISTENT FETAL VASCULATURE IN IDENTICAL TWINGIRLS

Introduction and Objective: Persistent fetal vasculature (PFV) previously known as persistent hyperplastic primary vitreous (PHPV) is a rare congenital malformation idiopathic attributed to impaired regression of the hyaloids vascularization during the embryonic period. Most cases are sporadic and unilateral, and only 2% bilateral. The objective of this report is t o show a case with bilateral persistent fetal vasculature (BPFV) in twin girls and its management. Case Description: Five years old twin girls present with difficulties while studying at school. They were born premature in 28 weeks with normal growth and development. Both were strabismus and the visual acuity was 1/60 with normal intraocular pressure in the beginning. Both segments with elevated posterior vitreous membrane from the optic nerve, retinal fol d, and Bergmeister papilla. Both received observation management with eye glasses, optical and non-optical low vision aids for low vision. Conclusion: Bilateral persistent fetal vasculature is a rare congenital malformation with variated clinical features. The management is surgery or observation depends on clinical, anatomy anomaly, and visual prognose. Children with BPFV growing niche with posterior anomaly roomates mostly related with poor visual prognostic. Bilateral persistent fetal vasculature needs of comprehensive management. Lifelong monitoring is a mandatory to avoid complications and visual rehabilitation due for daily living.