Giant choledochal cyst in 8 years old female

Abstract Background : Choledochal cyst incidence in Asian population is 1 : 1000 live births, and more common in female. The classic triad can be found in younger children is icteric, abdominal pain, and palpable mass in the abdomen. Various technique has been performed, but cyst excision and Roux-en-Y hepaticojejunostomy still prefered. Inappropriate management can cause complications such as pancreatitis, spontaneously cyst rupture, cholangiocarcinoma, and death during operation. Objective : To describe a rare case of Giant Choledocal Cyst Case : We report a case 8 years old female present with abdominal pain and a palpable mass in abdomen from below arcus costae to right inguinal region. Laboratory finding show serum bilirubin, alkaline phosphatase, gamma-glutamyl transferase (GGT) level are elevated. Computered tomography scan shows type IV choledochal cyst, with size 117.1 x 83.5 mm. First step surgery, external drainage already was performed to decrease the intraabdominal pressure. The definitive surgery was incomplete cyst excision and Roux-en-Y hepaticojejunostomy. The patient was discharged in good condition. The long-term prognostic of the patient is dubia ad bonam, biliary tract malignancy may still occur. Keywords : Giant Choledocal Cyst, Roux-en-Y hepaticojejunostomy